Evaluation of branched-chain amino acid intake in children with maple syrup urine disease and methylmalonic aciduria.
Journal of inherited metabolic disease1990Parsons HG, Carter RJ, Unrath M, et al.
Study designOther primary literature
SubjectHuman
Abstract
cc by 以外(cc by-nc / cc by-nc-nd / NONE 等)は抄録を再掲しない。DOI/PMID へのリンクのみ表示する。
MeSH
Amino Acid Metabolism, Inborn ErrorsAmino Acids, Branched-ChainAmmoniaBody WeightChild, PreschoolCreatinineDietary ProteinsFemaleFood, FormulatedGrowthHumansInfantInfant, NewbornIsoleucineLeucineMaleMalonatesMaple Syrup Urine DiseaseMethylmalonic AcidNutritional RequirementsValine