ZERO WORLD RESEARCHLiterature database on amino acids & organic acids

Enzymology of the branched-chain amino acid oxidation disorders: the valine pathway.

Journal of inherited metabolic disease2012Wanders RJ, Duran M, Loupatty FJ
Study designOther primary literature
SubjectHuman & animal

Abstract

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MeSH

Amino Acid Metabolism, Inborn ErrorsAmino Acids, Branched-ChainAnimalsEnoyl-CoA HydrataseHumansHydroxybutyrate DehydrogenaseMethylmalonate-Semialdehyde Dehydrogenase (Acylating)MitochondriaModels, ChemicalOxidoreductases Acting on CH-CH Group DonorsOxygenThiolester HydrolasesValine

DOI 10.1007/s10545-010-9236-x

PMID 21104317

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