Enzymology of the branched-chain amino acid oxidation disorders: the valine pathway.
Journal of inherited metabolic disease2012Wanders RJ, Duran M, Loupatty FJ
Study designOther primary literature
SubjectHuman & animal
Abstract
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MeSH
Amino Acid Metabolism, Inborn ErrorsAmino Acids, Branched-ChainAnimalsEnoyl-CoA HydrataseHumansHydroxybutyrate DehydrogenaseMethylmalonate-Semialdehyde Dehydrogenase (Acylating)MitochondriaModels, ChemicalOxidoreductases Acting on CH-CH Group DonorsOxygenThiolester HydrolasesValine