Leucine toxicity in a neuronal cell model with inhibited branched chain amino acid catabolism.
Brain research. Molecular brain research2004Kasinski A, Doering CB, Danner DJ
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MeSH
3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide)AnimalsApoptosisCell SurvivalDoxycyclineLeucineMaple Syrup Urine DiseaseMitochondriaModels, BiologicalNerve DegenerationNeuronsPC12 CellsProteinsRNA, MessengerRatsReaction TimeTransgenes
DOI 10.1016/j.molbrainres.2003.08.023
PMID 15010210
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